DSP and cardiomyopathy: Smith et al. [6] proposed the term “desmoplakin cardiomyopathy”, which describes a clinical phenotype characterized by a large amount of left ventricular fibrosis (typically assessed with cardiac magnetic resonance imaging and characterized by ring-like LGE patterns) [41] with normal left cardiac function, episodes of myocardial necrosis, and a significant degree of electrical instability.