In this study, ILD preceded vasculitis diagnosis in 22.1% of cases and mainly in p-ANCA positive patients (85.7%), while among those with c-ANCA, only one patient developed ILD before vasculitis (in 44.2% of cases the diagnoses were concomitant, and in 33.7% ILD followed the diagnosis of AAV). Here, PRTN3 is linked to vasculitis.