In a Caucasian family, a 14-year-old boy PCD-#12 II1, who demonstrated chronic maxillary sinusitis, adenoids, and bronchiectasis as well as total paralysis of ciliary apparatus (Additional file 16), harbored a 2-bp deletion variant c.79_80del in LRRC6 (Fig. 4B). Here, DNAAF11 is linked to bronchiectasis.