Additionally, the expression of GABAA subunits is diminished in the murine model of Rett syndrome (MeCP2+/- mouse brain) [46, 47] and the model of Fragile X syndrome (FMR1 knock-out mouse: α3, α4, β1, β2, γ1, γ2) [48–50]. This evidence concerns the gene MECP2 and atypical Rett syndrome.