Adding to the complexity, other neurodegenerative disorders such as PSP, Alzheimer’s disease (AD), TAR DNA-binding protein of 43 kDa (TDP-43) proteinopathy, and dementia with Lewy bodies (DLB) can present with CBS indistinguishable from that observed in CBD [5–7]. This evidence concerns the gene TARDBP and supranuclear palsy, progressive, 1.