A sensory ataxic neuropathy associated with a deletion in the mitochondrial tRNATyr gene has been described in golden retriever dogs [25], and cardiomyopathy and arrhythmia have been described in a family of Rhodesian ridgeback dogs with a missense variant in the nuclear gene QIl1 (also called MICOS13; OMIA# 001040-9615) [26]. Here, MICOS13 is linked to cardiomyopathy.