However, based on a recent revision of gene-disease associations, the list of MODY-causative genes should be restricted to the following: HNF4A, GCK, HNF1A, PDX1, HNF1B, NEUROD1, CEL, INS, ABCC8, KCNJ11, along with RFX6, recently proposed as an additional MODY gene [6]. Here, INS is linked to MODY.