Though the etiopathogenesis of MPCs is still largely unknown, recent studies have revealed some genetic abnormalities, such as platelet-derived growth factor receptor-beta (PDGFRB) mutations, NOTCH receptor 3 (NOTCH3) mutations, serum response factor, and NOTCH rearrangements as being associated with various pericytic tumors. Here, PDGFRB is linked to pericytic neoplasm.