Inactivating mutations in the NF2 gene, which codes for the tumor suppressor merlin, causes the autosomal-dominant tumor predisposition disorder of the nervous system NF2-related Schwannomatosis (NF2-SWN, formerly known as neurofibromatosis type 2) [[1], [2], [3]]. The gene discussed is NF2; the disease is NF2-related schwannomatosis.