Other non-classical/novel presentations without definitive/repeated antibody associations include whip-like or flagellate erythema (described in some individuals with anti-TIF1-γ antibodies but also in Case 6 with anti-NXP-2 disease), pityriasis rubra pilaris-like (Wong-type) DM, and perinasal swelling (16–18). This evidence concerns the gene TRIM33 and familial pityriasis rubra pilaris.