CMKLR1 and idiopathic pulmonary fibrosis: To confirm the translational relevance of CMKLR1 as a biomarker in fibrotic lung diseases, we demonstrated that high CMKLR1 expression by BAL cells is associated with a distinct IPF endotype with a significantly high mortality, in particular in the short-to-intermediate timeframe, and enrichment of inflammatory and ECM remodeling pathways.