The most common of this family of disorders is Aicardi Goutières Syndrome (AGS) (1–4), although there are other disorders including Familial Chilblain Lupus (FCL), STING-associated vasculopathy with onset in infancy (SAVI), and chronic atypical neutrophilic dermatosis with lipodystrophy and elevated temperatures (CANDLE) (5). Here, STING1 is linked to Aicardi-Goutieres syndrome.