Nevertheless, the identification of the lack of von Hippel Lindau (VHL) gene alterations, chromosome 3p35 loss, and trisomy 7/17, along with follow-up data indicating an indolent clinical behavior, with no evidence of any recurrence or metastasis so far, supported the name change from “carcinoma” to “tumor” in the new classification [7,8]. The gene discussed is VHL; the disease is neoplasm.