Progressive Myoclonic Epilepsy type 7, also known as myoclonus epilepsy and ataxia due to potassium channel mutation (MEAK), is associated with the recurrent c.959G > A (p.Arg320His) variant in KCNC1 and stands out for , relatively easily treatable epilepsy without severe cognitive impairment and autosomal dominant inheritance associated with de novo variants [1, 2]. Here, KCNC1 is linked to Progressive myoclonic epilepsy.