Mutations in the gap junction beta 2 protein (GJB2) gene, which encodes the protein connexin 26 and is involved in inner ear homeostasis, are found in approximately 50% of patients with autosomal recessive nonsyndromic hearing loss [2] and is one of the most important causes of prelingual nonsyndromic hearing loss in various populations [3]. Here, GJB2 is linked to hearing loss disorder.