Schwannomatosis is designated as SMARCB1-related, LZTR1-related, or 22q-related.66 Meningiomas are uncommon in non-NF2-related schwannomatosis and not part of the diagnostic criteria of LZTR1-related schwannomatosis and SMARCB1-related schwannomatosis despite the presence of SMARCB1 mutations in sporadic clear cell meningiomas.67 Meningiomas in NF2-SWN patients will be discussed in more detail in a later section. This evidence concerns the gene LZTR1 and schwannomatosis.