SDHB and von Hippel-Lindau disease: Indeed, four PGLs were diagnosed during screening for genetic syndromes (two patients affected by Von Hippel Lindau syndrome and another two patients with SDH germline mutation), and one patient had a known MEN2B-mutation; this patient was a young woman (32 years old) who had already undergone a total thyroidectomy for medullary thyroid carcinoma before abdominal surgery.