The presence of cytological and architectural atypia, an infiltrative growth pattern, a high Ki-67 index, diffuse strong p53 staining, BAP1 loss, and genomic alterations, such as IDH1/IDH2 mutation and FGFR2 fusion, favors ICCA [9]. The gene discussed is FGFR2; the disease is infantile convulsions and choreoathetosis.