OTULIN and autoinflammation, panniculitis, and dermatosis syndrome, autosomal recessive: Moreover, homozygous or compound heterozygous OTULIN variants cause an autoinflammatory disease called otulipenia or OTULIN-related autoinflammatory syndrome (ORAS) in an autosomal recessive fashion (Damgaard et al., 2016, 2019; Nabavi et al., 2019; Zhou et al., 2016; Zinngrebe et al., 2022).