We measured the expression of the main DNA repair genes previously described as modifiers in Huntington disease: MLH1 (MIM: 120436), MLH3 (MIM: 604395), MSH2 (MIM: 609309), MSH3 (MIM: 600887), MSH6 (MIM: 600678), PSM1 (MIM: 600258), PSM2 (MIM: 600259), LIG1 (MIM: 126391), and FAN1 (MIM: 613534).10 Here, MSH2 is linked to juvenile Huntington disease.