In addition to MYO7A, four genes encoding the tip-link complex, USH1C, SANS, CDH23 and PCDH15, are associated with Usher syndrome type 1 (Verpy et al., 2000; Ahmed et al., 2001; Alagramam et al., 2001; Bolz et al., 2001; Weil et al., 2003). Here, MYO7A is linked to Usher syndrome.