CTLA4 and autoimmune lymphoproliferative syndrome due to CTLA4 haploinsufficiency: The deficiency of CTLA-4 is known as CTLA-4 haploinsufficiency with autoimmune infiltration (CHAI), while LRBA defects are termed “LRBA deficiency with autoantibodies, regulatory T (Treg) cell defects, autoimmune infiltration, and enteropathy” (LATAIE), emphasizing immune dysregulation as a major feature [36].