In the Chinese population, nearly 50% of cases of NSHL are associated with mutations in the following genes: GJB2 (OMIM: 121011), GJB3 (OMIM: 603324), SLC26A4 (OMIM: 605646) and the mitochondrial gene MT-RNR1 (OMIM: 561000) [4]. Here, MT-RNR1 is linked to nodular sclerosis classical Hodgkin lymphoma.