Yano et al., Dundr et al., McCluggage et al., and Chapel et al. found that mesonephric-like adenocarcinomas and endometrial carcinomas, plasmacytoid junctional tumors, and low-grade plasmacytoid carcinomas of the ovary share common mutations in the KRAS and NRAS genes, which also supports the idea that mesonephric-like adenocarcinoma (MLA) is of the Mullerian origin [4–7]. Here, NRAS is linked to microphthalmia with limb anomalies.