In contrast, FXN GAA expanded repeats in Friedreich’s ataxia patients show an expansion bias in the cerebellum (De Biase et al. 2007), and skeletal muscle in Myotonic Dystrophy Type 1 present with much larger DMPK CTG expansions (Thornton et al. 1994). The gene discussed is FXN; the disease is Friedreich ataxia.