INS and Charlevoix-Saguenay spastic ataxia: These were present in the group of patients with SACS in 4.07% (n = 438), 11.6% (n = 1249), and 6.02% (n = 648) of cases, respectively; among the three groups, the highest OR value was attributed to the category treated with insulin therapy (OR of 1.12 and 95% CI of 1.03–1.21).