Electron microscopy (EM) has been useful in the diagnosis of AT and show long microvilli, tonofilaments, desmosomes and few micropinocytic vesicles.9,10 Molecular alteration of this tumour shows somatic missense mutation in TRAF7 gene that drives aberrant NF-Kb pathway activation.2 Whilst these ancillary study are important in the diagnosis of adenomatoid tumour, the microscopic features and immunohistochemical stains are enough to reach a diagnosis in most cases as was also evident in this study. The gene discussed is TRAF7; the disease is ataxia telangiectasia.