Patients with DBN carrying an FGF14 repeat expansion all exhibited additional cerebellar oculomotor signs (saccadic pursuit, dysmetric saccades, gaze‐evoked nystagmus, rebound nystagmus, impaired visual fixation suppression of the VOR), although only 43% displayed cerebellar ataxia despite protracted disease evolution. This evidence concerns the gene FGF14 and pathologic nystagmus.