FTD is a neuropathologically heterogeneous neurodegenerative disorder characterized by the presence in the brain of different proteins deposits, i.e., tau, ubiquitin, fused-in-sarcoma (FUS) protein, TAR DNA-binding protein 43 (TDP-43), and dipeptide repeat proteins in C9orf72 pathological expansion carriers, forming distinct inclusion bodies [6,7]. This evidence concerns the gene FUS and frontotemporal dementia.