Atp13a2 mice-Lipofuscin accumulation in CTX, HPC, CBL, BS-Increased ubiquitin inclusions-Increased GFAP in CTX, HPC, CLB-Increased Iba-1 in CTX, HPC, CBL, BSAtp13a2 Het-Lipofuscin accumulation in CTX-Increased GFAP and Iba-1 in CTX, HPC, BS. The gene discussed is ATP13A2; the disease is cerebrotendinous xanthomatosis.