There are reports of aneurysms that have formed after the normal PR3-ANCA level in this rare complication of the disease, and such aneurysms may occur independently of the activity of GPA itself.5) Aneurysm formation of any size is possible at any time during the course of GPA, although its incidence is low.2) Here, PRTN3 is linked to granulomatosis with polyangiitis.