MRPL18 and Barth syndrome: The CLPXP-relevant intermediate assemblies of the mtLSU have been described before [64,65,66,67,68,69], and the stress-dependent redistribution of the mitochondria-specific MRPL18-L38-L40-L46-L48-L55 cluster in complexomics profiles was reported for Barth syndrome as a consequence of mitochondrial cardiolipin anomalies [65,67,68].