This histopathologic variant of SS, first described by Requena et al. in 2005 [12], is characterized by a dermal infiltrate of mononuclear cells of histiocytic appearance, but strongly positive for myelocytic and promyelocytic markers, as demonstrated by the double immunostain for myeloperoxidase (MPO) and myeloid cell nuclear differentiation antigen (MNDA) [13]. This evidence concerns the gene MNDA and synovial sarcoma.