Angiofibromas are commonly found in the nasal cavity, orbit and eyelids.[12] Microscopically, it is shown as short spindle cells with unequal distributed and diffused thin-walled lobulated blood vessels in a mucous or glioidal background, on immunophenotyping, it expresses vimentin, CD31, CD34, in addition to myogenic antibodies.[13] Schwannoma is a benign tumor originating from Schwan cells that encases the peripheral nerves with an intact envelope. The gene discussed is PECAM1; the disease is Angiofibromas.