We summarized that patients with MODY13 had the following characteristics: (a) similar prevalence between males and females; (b) the onset age of nearly half of the patients >25 years old; (c) nonobese diabetes; (d) low FCP and different amino acid mutations did not affect the concentration of FCP; (e) mutation sites mostly concentrated in intracellular N‐ and C‐terminal domains of Kir6.2 and the majority of gene mutations causing MODY13 were from G to A; and (f) lower incidence rates of chronic complications than type 1 and type 2 diabetes. Here, KCNJ11 is linked to type 2 diabetes mellitus.