TMC1 and autosomal dominant nonsyndromic hearing loss 36: However, in the literature, most of the TMC1 variants are responsible for DFNB7/11, whereas only eight variants (p.Ser320Arg, p.Tyr381Asn, p.Gly417Arg, p.Met418Lys, p.Asp543Asn, p.Asp572Asn, p.Asp572His, p.Thr422Lys) are reported as causative for DFNA36 [16, 33, 43, 50–56].