Neutropenia also occurs in GATA2 deficiency patients (Pasquet et al., 2013) and inversions of the CD4/CD8 T cell ratio have been reported (Mutsaers et al., 2013; Ganapathi et al., 2015), indicating that GATA2 plays a crucial role as a key component within the BM hematopoietic hierarchy, orchestrating the differentiation and maintenance of diverse hematopoietic cell lineages. This evidence concerns the gene GATA2 and Decreased total neutrophil count.