In our attempt to model the limb-girdle muscular dystrophy type 2A (LGMD2A) with induced pluripotent stem cell-derived skeletal muscle cells and excluding at the same time any variance arising from the cell line genetic background, we intended to generate a hiPSC isogenic line from our LGMD2A patient-derived iPSC line (Figures 1(a) and 2). Here, CAPN3 is linked to autosomal recessive limb-girdle muscular dystrophy type 2A.