Delay and/or absence of central BAEP waves (described in detail in9, 26) were found in all dogs biallelic for the KCNJ10 variant, but not in the Parson Russell terrier biallelic for the CAPN1 variant,9, 26 nor in a dog with myokymia/neuromyotonia alone. Here, CAPN1 is linked to Isaacs syndrome.