All 21 dogs with spinocerebellar ataxia with myokymia or neuromyotonia were biallelic (homozygous) for the KCNJ10 c.627C>G variant (19 Jack Russell terriers, 1 Dachshund and 1 mixed breed; Table 1). The gene discussed is KCNJ10; the disease is cerebellar ataxia.