Various forms of tauopathies (Pick’s disease—PiD, corticobasal degeneration—CBD, progressive supranuclear palsy—PSP, argyrophilic grain disease—AGD, primary age-related tauopathy—PART, and neurofibrillary tangle-predominant dementia) commonly named as frontotemporal lobar degeneration with tau pathology (FTLD-tau) are characterized by cytoplasmic aggregates of phosphorylated tau [5,6]. The gene discussed is MAPT; the disease is tauopathy.