REN and Hyperkalemia: The Gordon syndrome (GS), also known as familial hyperkalemic hypertension (FHH), chloride shunt syndrome, or pseudo-hypoaldosteronism type II (PHAII) (MIM#145260), is an infrequent disorder associated with net positive Na+ balance and renal K+ retention resulting in hypertension, hyperkalemia, and hyperchloremic metabolic acidosis, low plasma renin (PR) activity, and usually normal plasma aldosterone (PA) levels.