Indeed, of the SANS and ADGRV1 mutations listed in the Human Gene Mutation Database (https://digitalinsights.qiagen.com/products-overview/clinical-insights-portfolio/human-gene-mutation-database/ (accessed on 9 March 2023)), more are reported as being linked to isolated deafness than to Usher Syndrome. The gene discussed is ADGRV1; the disease is deafness.