Friedrich's ataxia (FRDA), a monogenic recessive neurodegenerative condition, is characterized by progressive cerebellar and sensory ataxia, precipitated by the amplification of GAA repeats within the frataxin (FXN) gene, which encodes for the mitochondrial protein frataxin involved in iron-sulfur cluster biogenesis [804–806]. Here, FXN is linked to Friedreich ataxia.