PMEL and melanotic neurilemmoma: These tumors are benign and, therefore, the distinction from Malignant Peripheral Nerve Sheath Tumors (MPNSTs) is important.15, 16 Melanocytic schwannomas are recognized by the WHO as a distinct entity that rarely affects the CNs.17, 18 Melanocytic schwannomas are grossly pigmented and express melanocytic markers such as HMB45 and melan-A, leading to a distinct differential diagnosis that includes melanoma.