Four additional individuals (3%; #P29, #P30, #P31 and #P32 in Table 2) were found to carry biallelic mutations in MYO7A, causative of either Usher syndrome type 1B or DFNA2/11, yet syndromic features related with Usher syndrome could not be demonstrated. The gene discussed is MYO7A; the disease is Usher syndrome type 1B.