NPPB and pulmonary arterial hypertension: In addition to the basic parameters recommended by the ESC guidelines (NT-proBNP, 6MWT, WHO FC), the REVEAL 2.0 includes PAH etiology (+1 point for PAH-CTD), male age > 60 years old, estimated glomerular filtration rate (eGFR), heart rate, systolic blood pressure, all-cause hospitalizations ≤ 6 months, pericardial effusion on echocardiogram, percent predicted DLCO, mRAP and PVR.