However, there is a small number of individuals in whom a pathogenic variant in dolichyl-phosphate glucosyltransferase (ALG5), DnaJ homolog subfamily B member 11 (DNAJB11), or intraflagellar transport protein 140 homolog (IFT140) has been established as the cause of ADPKD [26,27,28,29,30]. Here, DNAJB11 is linked to autosomal dominant polycystic kidney disease.