SERPING1 and hereditary angioedema: In support of consideration and use as a proxy for C1-INH deficiency analysis, it is known that this ICD 10 code, in practice (diagnostic coding) is related to the following ORPHANET codes: ORPHA 528663 (AE acquired); ORPHA 528623 (hereditary AE), ORPHA 100050 (HAE Type 1), ORPHA 100051 (HAE Type 2), and with MS-DRG 40.0.