Although neurofibromatosis type 2 (NF2) is much less common than neurofibromatosis type 1 (NF1), NF2 is more commonly associated with meningiomas, with estimates that 45%–58% of NF2 patients harbor intracranial meningiomas and 20% harbor spinal meningiomas (24). Here, NF2 is linked to spinal meningioma.