Nodal EBV-positive T- and NK-cell lymphoma (primary nodal-EBV-TNKL) is now recognized as a distinct entity in 5th edition of the WHO lymphoma classification; previously, it was subsumed as a subtype under the entity of PTCL-NOS [4]. The gene discussed is TNKS2; the disease is mature T-cell and NK-cell non-Hodgkin lymphoma.